A case with Paget-Schrotter syndrome: A rare primary upper vein thrombosis

Çaǧirci G., ÖZDEMİR Ö., Boyaci A., Şaşmaz H., Kütük E.

Turk Kardiyoloji Dernegi Arsivi, vol.31, no.12, pp.789-792, 2003 (SCI-Expanded) identifier

  • Publication Type: Article / Article
  • Volume: 31 Issue: 12
  • Publication Date: 2003
  • Journal Name: Turk Kardiyoloji Dernegi Arsivi
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
  • Page Numbers: pp.789-792
  • Keywords: Deep vein thrombosis, Effort thrombosis, Paget-Schrotter syndrome
  • Lokman Hekim University Affiliated: No


Thrombosis of deep veins of the upper extremity (UEDVT) is quite rare, accounting for only 1-2% of deep vein thrombosis in the body. Primary UEDVT is a rare disorder that refers either to effort thrombosis or idiopathic UEDVT. Paget-Schrotter syndrome, effort thrombosis, was initially described in 1875 in the patients with spontaneous UEDVT, usually in their dominant arm, after a strenous activity. The heavy exertion causes microtrauma to the vessel intima and leads to activation of the coagulation cascade. Anticoagulation, the cornerstone of the therapy, helps to maintain patency of venous collaterals and reduces thrombus propagation. In this paper, we present a patient with well-developed collaterals, and could be treated with warfarin successfully. Paget-Schrotter syndrome should be considered in the differential diagnosis in a young patient admitted with pain and swelling of dominant upper extremity. Although the patient, presented in this paper, was treated with anticoagulation successfully, to prevent the complications such as post-thrombotic syndrome that may affect the health quality of these young patients, more aggressive treatments, such as thrombolysis, should be considered.